Congenital disorders (birth defects)
-
organ defects that occur during prenatal development of
the fetus and are present at birth. They affect to varying degrees about 3% of
newborns.
·
Atresia - congenital intestinal obstruction - it
may be just a persistent membrane in the lumen of the intestine that prevents
passage, or a complete disruption of intestinal continuity
·
Stenosis - narrowing of the intestinal lumen
·
Failure of rotation of the colon or its
attachment to the posterior abdominal wall - nonrotation, incomplete rotation
(cecum lies above the duodenojejunal junction) or reverse rotation (clockwise
rotation) - a common complication is volvulus and duodenal obstruction
·
Ladd's syndrome - bowel rotation disorder in
combination with congenital midgut volvulus and compression of the duodenum by
a non-rotated cecum
Miroslav Zeman,
Zdeněk Krška, coll. Special surgery.
2014
·
Isolated high cecal position - this is an
incomplete rotation of the cecum, which is located in the right hypochondrium
(this birth disorder can be clinically completely silent)
·
Hirschprung's disease - is caused by the absence
of ganglion cells (plexus myentericus Auerbachi and plexus submucosus
Meissneri) in the wall of the large intestine in various extent - from
m.sphincter ani internus proximally. This leads to stenosis of the affected
segment and dilatation of the bowel above this segment (up to megacolon
congenitum). The first clinical sign is usually delayed meconium passage, in
some children the first symptom is chronic obstipation
Miroslav Zeman,
Zdeněk Krška, coll. Special surgery. 2014